(Last Updated On: October 30, 2018)

Authors: Mary Rose Lim-del Mindo MD, DPDS and Daisy King-Ismael MD, FPDS

Abstract

Pyoderma gangrenosum (PG) is a rare, inflammatory, ulcerative skin condition characterized by an ulcer with advancing violaceous border, negative cultures, unresponsiveness to antibiotics, the phenomenon of pathergy and histopathology showing neutrophilic infiltration. It usually occurs in all age groups but is rare among infants and very young children. A 6-month-old boy presented with papules which evolved into necrotic ulcers on the ears, perioral area, nose, neck, inguinal, scrotal, intergluteal and genital areas. The destruction of the ear cartilage made the clinical picture unusual and to the best of our knowledge, has rarely been reported as a feature of pyoderma gangrenosum in published case reports. The patient responded well to Hydrocortisone IV and tapering doses of oral prednisone. The long term effects in patients who developed infantile PG are still unknown and further follow-up of these unusual cases is recommended.

 

Citation

Lim-del Mindo, MR & King-Ismael, D. (2017). Mutilating pyoderma gangrenosum in an infant: A case report. Journal of the Philippine Dermatological Society, 26(1), 62-64.

 

Keywords

Pyoderma Gangrenosum, neutrophilic dermatosis, pediatric dermatology

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