(Last Updated On: April 2, 2019)

Authors: Nenita Q. Manzano, MD, FPDS, Jo Faustine Manzano, MD, Johannes F. Dayrit, MD, FPDS

Abstract

Mycosis fungoides (MF) is an epidermotropic, primary cutaneous T-cell lymphoma (CTCL) composed of small to medium-sized T-lymphocytes with cerebriform nuclei and with a T-helper phenotype.1 This is the most common type of cutaneous lymphoma, which represents almost 50% of all lymphomas arising in the skin.1-3 The incidence of MF is approximately 0.36 per 100,000 person-years in the United States.4-5
Pigmented purpuric dermatosis (PPD) is a general term that is used to describe a group of chronic and relapsing cutaneous lesions of unknown etiology. This is characterized by petechiae and pigmentary macules of the lower limbs.6, 7 Mycosis fungoides may present in various forms as
there are atypical variants that have been described in literature, one of the rare forms is the pigmented-purpura like MF.8 Mycosis fungoides clinically presenting as PPD was also described in a renal transplant patient.

 

Citation

Manzano NQ, Manzano J, Dayrit J. Pigmented purpuric dermatosis (PPD)-like mycosis fungoides on the leg of a Filipino male. J Phil dermatol Soc. 2018; 27(2):99-100.

 

Keywords

Mycosis fungoides, epidermotropic, T-cell lymphoma

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